Dermatomyositis-like syndrome in X-linked hypogammaglobulinemia. Case-report and review of the literature.

Authors

  • A Thyss
  • P el Baze
  • J C Lefebvre
  • M Schneider
  • J P Ortonne

DOI:

https://doi.org/10.2340/0001555570309313

Abstract

A case of dermatomyositis-like syndrome is described in a 19-year-old man with a history of Bruton's hypogammaglobulinemia. Although the patient had central-nervous-system manifestations (seizures), no echovirus was isolated in the cerebrospinal fluid, in contrast to previously reported cases. Data for our case and the 15 cases previously reported in the literature are reviewed. HLA typing of our patient revealed the presence of HLA B8 and DR3, which seems to play a major role in juvenile dermatomyositis.

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Published

1990-07-01

How to Cite

Thyss, A., el Baze, P., Lefebvre, J. C., Schneider, M., & Ortonne, J. P. (1990). Dermatomyositis-like syndrome in X-linked hypogammaglobulinemia. Case-report and review of the literature. Acta Dermato-Venereologica, 70(4), 309–313. https://doi.org/10.2340/0001555570309313

Issue

Section

Articles