Swelling of the Left Upper Limb with Red Papules, Necrosis and Crusting: A Quiz

Authors

  • Jia-Wei Liu Department of Dermatology, State Key Laboratory of Complex Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, National Clinical Research Center for Dermatologic and Immunologic, Beijing, China.
  • Jie Zhang Department of Dermatology, State Key Laboratory of Complex Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, National Clinical Research Center for Dermatologic and Immunologic, Beijing, China.
  • Hong-Zhong Jin Department of Dermatology, State Key Laboratory of Complex Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, National Clinical Research Center for Dermatologic and Immunologic, Beijing, China.

DOI:

https://doi.org/10.2340/actadv.v106.adv-2025-0120

Keywords:

skin neoplasm, diagnosis, histopathology, rare disease, epithelioid sarcoma, rare cancer, distal-type epithelioid sarcoma, pathology, Skin histology

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References

Czarnecka AM, Sobczuk P, Kostrzanowski M, Spalek M, Chojnacka M, Szumera-Cieckiewicz A, et al. Epithelioid sarcoma – from genetics to clinical practice. Cancers 2020; 12: 2112. DOI: https://doi.org/10.3390/cancers12082112

Chase DR, Enzinger FM. Epithelioid sarcoma. Diagnosis, prognostic indicators, and treatment. Am J Surg Pathol 1985; 9: 241–263. DOI: https://doi.org/10.1097/00000478-198504000-00001

Spillane AJ, Thomas JM, Fisher C. Epithelioid sarcoma: the clinicopathological complexities of this rare soft tissue sarcoma. Ann Surg Oncol 2000; 7: 218–225. DOI: https://doi.org/10.1007/BF02523657

Guillou L, Wadden C, Coindre JM, Krausz T, Fletcher CD. “Proximal-type” epithelioid sarcoma, a distinctive aggressive neoplasm showing rhabdoid features. Clinicopathologic, immunohistochemical, and ultrastructural study of a series. Am J Surg Pathol 1997; 21: 130–146. DOI: https://doi.org/10.1097/00000478-199702000-00002

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Hornick JL, Dal Cin P, Fletcher CDM. Loss of INI1 expression is characteristic of both conventional and proximal-type epithelioid sarcoma. Am J Surg Pathol 2009; 33: 542–550. DOI: https://doi.org/10.1097/PAS.0b013e3181882c54

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Wolf PS, Flum DR, Tanas MR, Rubin BP, Mann GN. Epithelioid sarcoma: the University of Washington experience. Am J Surg 2008; 196: 407–412. DOI: https://doi.org/10.1016/j.amjsurg.2007.07.029

Alves A, Constantinidou A, Thway K, Fisher C, Huang P, Jones RL. The evolving management of epithelioid sarcoma. Eur J Cancer Care 2021; 30: e13489. DOI: https://doi.org/10.1111/ecc.13489

Gounder MM, Merriam P, Ratan R, Patel SR, Chugh R, Villalobos VM, et al. Real-world outcomes of patients with locally advanced or metastatic epithelioid sarcoma. Cancer 2021; 127: 1311–1317. DOI: https://doi.org/10.1002/cncr.33365

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Published

2026-05-25

How to Cite

Liu, J.-W., Zhang, J., & Jin, H.-Z. (2026). Swelling of the Left Upper Limb with Red Papules, Necrosis and Crusting: A Quiz. Acta Dermato-Venereologica, 106, adv–2025. https://doi.org/10.2340/actadv.v106.adv-2025-0120

Issue

Vol. 106 (2026)

Section

Quiz

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