Histiocytic medullary reticulosis presenting as Mucha-Habermann disease
DOI:
https://doi.org/10.2340/00015555585764Abstract
Histiocytic medullary reticulosis (HMR) is a rare, progressive, fatal reticuleondothelial proliferative disorder. It was diagnosed in a 10-year-old boy who had pityriasis lichenoides et varioliformis acuta of Mucha-Haberman which was controlled by dapsone for 2 years. One month after cessation of dapsone therapy, cutaneous tumors associated with fever, lymphadenopathy, and hepatosplenomegaly developed. Tissue biopsy specimens of skin, liver, spleen, lymph nodes, and a bone marrow aspirate demonstrated histiocytic erythrophagocytosis and atypical histiocytosis compatible with HMR. A rapidly progressing, fatal course followed despite intensive chemotherapy.Downloads
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Published
1978-01-01
How to Cite
Freeman, M., Taylor, J., Levin, H., Dyment, P., & Bergfeld, W. (1978). Histiocytic medullary reticulosis presenting as Mucha-Habermann disease. Acta Dermato-Venereologica, 58(1), 57–64. https://doi.org/10.2340/00015555585764
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