Nephrogenic Fibrosing Dermopathy: Report of Two Cases

Authors

  • Nádia Barbosa Aires
  • Mírian N. Sotto
  • Marcello M.S. Nico

DOI:

https://doi.org/10.2340/00015555-0296

Keywords:

nephrogenic fibrosing dermopathy, scleromyxoedema-like cutaneous disease, kidney transplantation.

Abstract

Nephrogenic fibrosing dermopathy is a recently described fibrosing disorder that emerges in different settings of renal insufficiency. The degree and cause of the underlying renal impairment seem not to be related to the severity of the nephrogenic fibrosing dermopathy. Lesions are typically symmetrical and usually develop on the limbs and trunk. These are characterized by skin-coloured to erythematous papules that coalesce into plaques markedly thickened in texture. Flexion contractures of the joints may be a feature of the disease. There is no consistently effective therapy for nephrogenic fibrosing dermopathy. We report here 2 Brazilian patients in connection with a short review. Remission was recorded in one case after plasmapheresis.

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Published

2007-08-09

How to Cite

Barbosa Aires, N., Sotto, M. N., & Nico, M. M. (2007). Nephrogenic Fibrosing Dermopathy: Report of Two Cases. Acta Dermato-Venereologica, 87(6), 521–524. https://doi.org/10.2340/00015555-0296

Issue

Section

Articles