Erythropoietic protoporphyria and terminal hepatic failure.
DOI:
https://doi.org/10.2340/0001555576453456Abstract
We report on a 44-year-old patient with erythropoietic protoporphyria who could effectively control his photosensitivity for 22 years with oral carotinoids. The clinical course of his disorder was complicated by liver involvement, initially expressed as marginally raised serum transaminase levels for several years. Terminal hepatic failure with fatal outcome developed 22 years after manifestation of his liver function abnormalities. Hepatic involvement represents an inconstant and unpredictable feature of erythropoietic protoporphyria, determining the prognosis of an otherwise clinically benign disorder.Downloads
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Published
1996-11-01
How to Cite
Bruch-Gerharz, D., Bolsen, K., Gerharz, C., & Goerz, G. (1996). Erythropoietic protoporphyria and terminal hepatic failure. Acta Dermato-Venereologica, 76(6), 453–456. https://doi.org/10.2340/0001555576453456
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